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Intravitreal injection of ranibizumab in severe retinopathy of incontinentia pigmenti  期刊论文  

  • 编号:
    080aca0b-f2e1-4a02-b1d0-ce2efba38e2e
  • 作者:
    Ni, Yingqin(倪颖勤)#[1,2]Huang, Xin(黄欣)*[1,2]Ruan, Lu[1,2];Xue, Kang(薛康)[1,2]Yu, Jia[1,2];Peng, Jie[3];Zhao, Peiquan[3];
  • 语种:
    English
  • 期刊:
    JOURNAL OF AAPOS ISSN:1091-8531 2018 年 22 卷 4 期 (325 - 327) ; AUG
  • 收录:
  • 摘要:

    Incontinentia pigmenti (IP) is a rare X-linked multisystem disorder that mainly affects females and is usually lethal to males in utero. Mutations in the NEMO gene on chromosome Xq28 (IKBKG, inhibitor of kB kinase gamma) have been shown to cause IP. Approximately 35% of patients have ophthalmic manifestations, and 20% develop vision-threatening diseases. Retinal vascular abnormalities, from peripheral retinal avascularity to neovascular proliferation, have been described in IP patients. Laser photocoagulation and cryotherapy are traditionally effective therapy for retinopathy of IP. Flow ever, some cases still progress to retinal detachment. We report 2 cases of IP infants treated with intravitreal ranibizumab with subsequent resolution of the vasculopathy.

  • 推荐引用方式
    GB/T 7714:
    Ni Yingqin,Huang Xin,Ruan Lu, et al. Intravitreal injection of ranibizumab in severe retinopathy of incontinentia pigmenti [J].JOURNAL OF AAPOS,2018,22(4):325-327.
  • APA:
    Ni Yingqin,Huang Xin,Ruan Lu,Xue Kang,&Zhao Peiquan.(2018).Intravitreal injection of ranibizumab in severe retinopathy of incontinentia pigmenti .JOURNAL OF AAPOS,22(4):325-327.
  • MLA:
    Ni Yingqin, et al. "Intravitreal injection of ranibizumab in severe retinopathy of incontinentia pigmenti" .JOURNAL OF AAPOS 22,4(2018):325-327.
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