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Successful treatment of kaposiform lymphangiomatosis with sirolimus 期刊论文

编号：

e6752461-0750-4686-934e-4e78f045f8a3
作者：

Wang, Zuopeng^[1] Li, Kai^[1] Yao, Wei^[1] Dong, Kuiran^[1] Xiao, Xianmin^[1] Zheng, Shan^[1]
语种：

English
期刊：

PEDIATRIC BLOOD & CANCER ISSN：1545-5009 2015 年 62 卷 7 期 (1291 - 1293) ; JUL
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关键词：

generalized lymphatic anomaly kaposiform lymphangiomatosis sirolimus vascular malformation
摘要：

Generalized lymphatic anomaly (GLA) is a rare and often fatal congenital lymphatic disorder that also commonly affects bone. Kaposiform lymphangiomatosis (KLA) is a novel subtype of GLA with poor prognosis and no proper treatment guidelines. A 9-year-old male with recurrent pleural effusion was clinically diagnosed as KLA. Following sirolimus therapy at a dose of 0.8mg/m(2) twice daily, pleural effusion was significantly decreased and the general status of the patient markedly improved. The clinical course indicates that sirolimus may present an effective therapeutic option in KLA. Moreover, KLA should be considered in differential diagnosis for cases of GLA with coagulopathy. Pediatr Blood Cancer 2015;62:1291-1293. (c) 2015 Wiley Periodicals, Inc.
推荐引用方式
GB/T 7714：

Wang Zuopeng,Li Kai,Yao Wei, et al. Successful treatment of kaposiform lymphangiomatosis with sirolimus [J].PEDIATRIC BLOOD & CANCER,2015,62(7):1291-1293.
APA：

Wang Zuopeng,Li Kai,Yao Wei,Dong Kuiran,&Zheng Shan.(2015).Successful treatment of kaposiform lymphangiomatosis with sirolimus .PEDIATRIC BLOOD & CANCER,62(7):1291-1293.
MLA：

Wang Zuopeng, et al. "Successful treatment of kaposiform lymphangiomatosis with sirolimus" .PEDIATRIC BLOOD & CANCER 62,7(2015):1291-1293.

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